Pulmonary Arterial Hypertension (PAH) is a rare blood vessel disorder of the lung in which the pressure in the pulmonary artery (the blood vessel that leads from the heart to the lungs) rises above normal levels and may become life threatening.
As the symptoms of this disease are rather common, PAH is usually mistaken for asthma.
These tests are necessary in order for the doctor to assess your pulmonary arterial pressure and to determine the cause if the pressures are high.
PAH has a poor prognosis and must be investigated. Patients who have symptoms need to be treated early. Outcomes of the treatment is largely dependent on the cause of the disease. Treatment with PAH specific therapy has been shown to improve symptoms, exercise capacity and overall prognosis of the disease.